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Supporting Information Additional Supporting Information may be found in the online version of this article: Table S1. Types of congenital neutropenia or functional defects described in the review
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Phagocytic neutrophil granulocytes are among the first immune cells active at sites of infection, forming an important first‐line defense against invading microorganisms. Congenital immune defects concerning these phagocytes may be due to reduced neutrophil numbers or function. Management of affected patients depends on the type and severity of disease. Here, we provide an overview of causes and treatment of diseases associated with congenital neutropenia, as well as defects of the phagocytic respiratory burst.
Pediatric Allergy and Immunology – Wiley
Published: Mar 1, 2017
Keywords: ; ; ; ; ; ;
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