Access the full text.
Sign up today, get DeepDyve free for 14 days.
Frederick Homer, C. Streamer (1956)
Effect of a phenylalanine-restricted diet on patients with phenylketonuria; clinical observations in three cases.Journal of the American Medical Association, 161 17
H. Bickel , J. Gerrard (1954)
Influence of Phenylalanine Intake on Chemistry and Behaviour of a Phenylketonuric ChildActa Paediat., 43
M. Armstrong, F. Tyler (1955)
Studies on phenylketonuria. I. Restricted phenylalanine intake in phenylketonuria.The Journal of clinical investigation, 34 4
H. Bickel, J. Gerrard, E. Hickmans (1954)
The Influence of Phenylalanine Intake on the Chemistry and Behaviour of a Phenylketonuria ChildActa Pædiatrica, 43
F. H. Tyler (1954)
Diseases of Nervous System: Metabolic Aspects of Some Neurological and Muscular DisordersAnn. Rev. Med., 5
N. L. Low , M. D. Armstrong (1956)
Two Unusual CasesLancet, 2
G. A. Jervis (1937)
Phenylpyruvic Oligophrenia: Introductory Study of 50 Cases of Mental Deficiency Associated with Excretion of Phenylpyruvic AcidArch. Neur. & Psychiat., 38
L. Woolf, R. Griffiths, A. Moncrieff (1955)
Treatment of Phenylketonuria with a Diet Low in PhenylalanineBritish Medical Journal, 1
Marvin Armstrong, Niels Low, James Bosma (1957)
Studies on phenylketonuria. IX. Further observations on the effect of phenylalanine-restricted diet on patients with phenylketonuria.The American journal of clinical nutrition, 5 5
M. D. Armstrong (1956)
Studies on Phenylketonuria: V.Proc. Soc. Exper. Biol. & Med., 93
F. A. Horner (1956)
Effect of a Phenylalanine-Restricted Diet on Patients with PhenylketonuriaJ. A. M. A., 161
Abstract In an earlier paper two of us (F. A. H. and C. W. S.) presented the short-term psychological and behavioral changes observed in two preschool phenylketonuric children treated with a phenylalanine-restricted diet.1 In addition, a newborn sibling of one of the cases, who had received dietary treatment since 8 weeks of age, was reported as developing normally through the first 9 months of life. The present paper offers an additional year of follow-up on these three patients. It also reports on the changes observed in a second newborn and two 18-month-old children under long-term therapy. Dietary Program The phenylalanine-restricted diet used in this series is that outlined by Armstrong and Tyler.2,3 Patients are given a phenylalanine-free diet consisting of a protein hydrolysate basal mix* (4.2 gm/kg/day), fat in the form of a vegetable oil (3.0 gm/kg/day) and CHO (10 gm/kg/day) for three weeks. On such a diet References 1. Horner, F. A., and Streamer, C. W.: Effect of a Phenylalanine-Restricted Diet on Patients with Phenylketonuria , J. A. M. A. 161:1628 ( (Aug. 25) ) 1956.Crossref 2. Tyler, F. H., and Armstrong, M. D.: Diseases of Nervous System: Metabolic Aspects of Some Neurological and Muscular Disorders , Ann. Rev. Med. 5:207, 1954.Crossref 3. Armstrong, M. D., and Tyler, F. H.: Studies on Phenylketonuria: I. Restricted Phenylalanine Intake in Phenylketonuria , J. Clin. Invest. 34:565 ( (April) ) 1955.Crossref 4. Armstrong, M. D., and Binkley, E. L.: Studies on Phenylketonuria: V. , Proc. Soc. Exper. Biol. & Med. 93:418 ( (Dec.) ) 1956. 5. Jervis, G. A.: Phenylpyruvic Oligophrenia: Introductory Study of 50 Cases of Mental Deficiency Associated with Excretion of Phenylpyruvic Acid , Arch. Neur. & Psychiat. 38:944 ( (Nov.) ) 1937. 6. Bickel, H.; Gerrard, J., and Hickmans, E. M.: Influence of Phenylalanine Intake on Chemistry and Behaviour of a Phenylketonuric Child , Acta Paediat. 43:64 ( (Jan.) ) 1954. 7. Woolf, L. I.; Griffiths, R., and Moncrieff, A.: Treatment of Phenylketonuria with a Diet Low in Phenylalanine , Brit. M. J. 1:57 ( (Jan. 8) ) 1955. 8. Berendes, H.: Paper presented at Western Society for Pediatric Research, Fourth Annual Meeting, Salt Lake City, October, 1956. 9. Low, N. L.; Armstrong, M. D., and Carlisle, J. W.: Phenylketonuria: Two Unusual Cases , Lancet 2:917 ( (Nov. 3) ) 1956.
A.M.A. Journal of Diseases of Children – American Medical Association
Published: Jun 1, 1957
Read and print from thousands of top scholarly journals.
Already have an account? Log in
Bookmark this article. You can see your Bookmarks on your DeepDyve Library.
To save an article, log in first, or sign up for a DeepDyve account if you don’t already have one.
Copy and paste the desired citation format or use the link below to download a file formatted for EndNote
Access the full text.
Sign up today, get DeepDyve free for 14 days.
All DeepDyve websites use cookies to improve your online experience. They were placed on your computer when you launched this website. You can change your cookie settings through your browser.